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Scleromyxedema (also known as lichen myxedematosus, papular mucinosis or paraproteinemia associated desmoplasia ) is a rare and chronic fibromucinous connective tissue disorder of unknown etiology. It is characterized by the presence of infiltrative skin lesions with deposits of mucinous material in the papillary dermis and the presence of a monoclonal protein 1gG-Kappa (abnormal paraprotein). There can be systemic involvement that is life-threatening. Thus far drug therapy for this condition, which has a high rate of morbidity, has not proven 100% effective. Condition may improve with various drug treatments but oftentimes will return or worsen.
Because there are very few Web resources that help define and explain scleromyxedema, Scleromyxedema Survivors aims to educate and inform, support and sympathize with people suffering from this disease. |
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